Laryngeal adenoid cystic carcinoma

case report

Authors

  • André Del Negro Faculdade de Ciências Médicas da Universidade Estadual de Campinas
  • Edson Ichihara Faculdade de Ciências Médicas da Universidade Estadual Campinas
  • Alfio José Tincani Faculdade de Ciências Médicas da Universidade Estadual de Campinas
  • Albina Altemani Faculdade de Ciências Médicas da Universidade Estadual de Campinas
  • Antônio Santos Martins Faculdade de Ciências Médicas da Universidade Estadual de Campinas

Keywords:

Adenoid cystic carcinoma, Larynx, Salivary gland, Radiotherapy, Laryngectomy

Abstract

CONTEXT: Adenoid cystic carcinomas are malignant tumors that occur in both the major and the minor salivary glands. A laryngeal location is rare because of the paucity of accessory salivary glands in this area. Adenoid cystic carcinomas account for less than 1% of all malignant tumors in the larynx, and only about 120 cases have been reported in the literature. These tumors have a slight female predisposition, and their peak incidence is in the fi fth and sixth decades of life. In this article, we describe a case of laryngeal adenoid cystic carcinoma and discuss its clinical characteristics and treatment. CASE REPORT: We report on a case of laryngeal adenoid cystic carcinoma in a 55 year-old female patient who presented with dyspnea and hoarseness. Features of the diagnostic and therapeutic evaluation are described and the clinical management of such cases is outlined. The clinical course, defi nitive treatment strategy and surgical procedure, and also adjuvant treatment with irradiation are discussed. Although the tumor is radiosensitive, it is not radiocurable.

Downloads

Download data is not yet available.

Author Biographies

André Del Negro, Faculdade de Ciências Médicas da Universidade Estadual de Campinas

MD. Attending surgeon, Head and Neck Service, Department of Surgery, Faculdade de Ciências Médicas da Universidade Estadual de Campinas, Campinas (FCM-Unicamp), São Paulo, Brazil.

Edson Ichihara, Faculdade de Ciências Médicas da Universidade Estadual Campinas

 

Undergraduate student, Faculdade de Ciências Médicas da Universidade Estadual de Campinas (FCM-Unicamp), Campinas, São Paulo, Brazil.

Alfio José Tincani, Faculdade de Ciências Médicas da Universidade Estadual de Campinas

MD, PhD. Assistant professor, Head and Neck Service, Department of Surgery, Faculdade de Ciências Médicas da Universidade Estadual de Campinas (FCM-Unicamp), Campinas, São Paulo, Brazil.

Albina Altemani, Faculdade de Ciências Médicas da Universidade Estadual de Campinas

MD, PhD. Assistant professor, Department of Pathology, Faculdade de Ciências Médicas da Universidade Estadual de Campinas (FCM-Unicamp), Campinas, São Paulo, Brazil.

Antônio Santos Martins, Faculdade de Ciências Médicas da Universidade Estadual de Campinas

MD, PhD. Chief, Head and Neck Service, Department of Surgery, Faculdade de Ciências Médicas da Universidade Estadual de Campinas (FCMUnicamp), Campinas, São Paulo, Brazil.

References

Javadi M, Bafrouee FM, Mohseni M, Asghari A. Laryngeal adenoid cystic carcinoma in a child: a case report. Ear Nose Throat J. 2002;81(1):34-5.

Morais Pérez D, Cortejoso Hernández A, Borau Clavero M, Martín Sigüenza G. Carcinoma adenoide quístico de laringe. [Adenoid cystic carcinoma of the larynx]. Acta Otorrinolaringol Esp. 1999;50(8):660-3.

Dexemble P, Huth J, Rebufy M, Chabrol A. Carcinome adénoïde kystique du larynx. A propos de deux cas. [Cystic adenoid carcinoma of the larynx: two cases]. Ann Otolaryngol Chir Cervicofac. 2003;120(4):244-8.

Tincani AJ, Del Negro A, Araújo PP, et al. Management of salivary gland adenoid cystic carcinoma: institutional experience of a case series. Sao Paulo Med J. 2006;124(1):26-30.

Kufeld M, Junker K, Sudhoff H, Dazert S. Kollisionstumor eines adenoidzystischen Karzinoms des Hypopharynx und eines Plat- tenepithelkarzinoms des Larynx. [Collision tumor of a hypopha- ryngeal adenoidcystic carcinoma and a laryngeal squamous cell carcinoma]. Laryngorhinootologie. 2004;83(1):51-4.

Olofsson J, van Nostrand AW. Adenoid cystic carcinoma of the larynx: a report of four cases and a review of the literature. Cancer. 1977;40(3):1307-13.

Downloads

Published

2007-09-09

How to Cite

1.
Negro AD, Ichihara E, Tincani AJ, Altemani A, Martins AS. Laryngeal adenoid cystic carcinoma: case report. Sao Paulo Med J [Internet]. 2007 Sep. 9 [cited 2025 Oct. 16];125(5):295-6. Available from: https://periodicosapm.emnuvens.com.br/spmj/article/view/2156

Issue

Section

Case Report