Treatment of Fraley’s syndrome by upper-pole nephrectomy

Authors

  • Thaís Bandeira Cerqueira Escola Bahiana de Medicina e Saúde Pública and Santa Casa de Misericórdia da Bahia
  • Natalia Bacellar Costa Lima Escola Bahiana de Medicina e Saúde Pública and Santa Casa de Misericórdia da Bahia
  • Romeu Magno Baptista Neto Escola Bahiana de Medicina e Saúde Pública and Santa Casa de Misericórdia da Bahia
  • José Cohim Moreira Filho Escola Bahiana de Medicina e Saúde Pública and Santa Casa de Misericórdia da Bahia
  • Luiz Eduardo Café Escola Bahiana de Medicina e Saúde Pública and Santa Casa de Misericórdia da Bahia

Keywords:

Nephrectomy, Kidney diseases, Kidney calculi, Hydronephrosis, Low back pain

Abstract

CONTEXT: Fraley’s syndrome is characterized by vascular compression on the superior infundibulum with secondary dilatation of the upper pole calyx, mostly located on the right side. CASE REPORT: We present the case of a 22-year-old woman with vascular compression of the upper-pole infundibulocalyceal system (Fraley’s syndrome). The patient had a history of frequent hospitalizations for emergency care due to lumbar pain over the past twelve months. The diagnosis was obtained following renal arteriography. Since the surgical treatment by means of upper-pole nephrectomy, the patient has not had any further symptoms.

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Author Biographies

Thaís Bandeira Cerqueira, Escola Bahiana de Medicina e Saúde Pública and Santa Casa de Misericórdia da Bahia

Undergraduate medical student, Escola Bahiana de Medicina e Saúde Pública (EBMSP), Salvador, Bahia, Brazil.

Natalia Bacellar Costa Lima, Escola Bahiana de Medicina e Saúde Pública and Santa Casa de Misericórdia da Bahia

Undergraduate medical student, Escola Bahiana de Medicina e Saúde Pública (EBMSP), Salvador, Bahia, Brazil.

Romeu Magno Baptista Neto, Escola Bahiana de Medicina e Saúde Pública and Santa Casa de Misericórdia da Bahia

MD. Urologist, Urology Service, Santa Casa de Misericórdia da Bahia, Salvador, Bahia, Brazil.

José Cohim Moreira Filho, Escola Bahiana de Medicina e Saúde Pública and Santa Casa de Misericórdia da Bahia

MD. Urologist, Urology Service, Santa Casa de Misericórdia da Bahia, Salvador, Bahia, Brazil.

Luiz Eduardo Café, Escola Bahiana de Medicina e Saúde Pública and Santa Casa de Misericórdia da Bahia

MD, PhD. Adjunct professor, Escola Bahiana de Medicina e Saúde Pública (EBMSP), and Head of Urology Service, Santa Casa de Misericórdia da Bahia, Salvador, Bahia, Brazil.

References

Fraley EE. Vascular obstruction of superior infundibulum causing nephralgia. A new syndrome. N Engl J Med. 1966;275(25):1403-9.

D’Amico A, Lusuardi L, Ficarra V, et al. Experience in the surgical treatment of Fraley’s syndrome. Eur Urol. 2000;38(4):410-4.

Fazeli-Matin S, Streem SB Nephron sparing manage- ment of Fraley’s syndrome with a pyelopyelostomy. J Urol. 1998;159(2):487-9.

Fernández Arjona M, Tagarro D, Moyano Calvo JL, Rabadán Ruiz M, Herrero Torres L, Pereira Sanz I. Tratamiento percutá- neo del síndrome de Fraley. [Percutaneous treatment of Fraley syndrome]. Arch Esp Urol. 1996;49(1):55-8.

Biocic M, Saraga M, Maskovic J, Vukic-Kosuljandic D, Saraga- Babic M, Budimir D. A nephron-sparing surgical procedure for Fraley’s syndrome. A case report. Eur J Pediatr Surg. 2002;12(5):341-4.

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Published

2007-11-11

How to Cite

1.
Cerqueira TB, Lima NBC, Baptista Neto RM, Moreira Filho JC, Café LE. Treatment of Fraley’s syndrome by upper-pole nephrectomy. Sao Paulo Med J [Internet]. 2007 Nov. 11 [cited 2025 Oct. 16];125(6):354-5. Available from: https://periodicosapm.emnuvens.com.br/spmj/article/view/2181

Issue

Section

Case Report